- Original Article
- Comparison of the Effects of Portacaval Shunt and Dietary therapy in Type I Gyocogen Storagy Diseases(GSD).
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Dong Hyun Ju, Sei Won Yang, Hyung Ro Moon
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Clin Exp Pediatr. 1988;31(6):762-771. Published online June 30, 1988
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Type I GSD is a metabolic disease resulted from defective glucose-6-phosphatase activities in liver,
kindey and intestine. They are characterized by growth retardation, enlargement of liver and kidney,
hypoglycemia, hyperuricemia, and hyperlipidemia.
Various methods were suggested for the management of GSD. They are night-time nasogastric
feeding of glucose solution with frequent day-time feeding, intravenous hyperalimentation, cornstarch
therapy end-to-side portacaval shunt, etc.
In this study, the effects... |
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